The anhidrotic ectodermal dysplasia or Christ-Siemens-Touraine syndrome is a scarce pathology, characterized by abnormalities occuring during the morphogenesis of tissues and organs of ectodermal origin, induced by genetic disorders. This syndrome is characterized by the classic symptomatic triad: anhidrosis / hypohidrosis, anodontia / hypodontia, hypotrichosis (4). Dental abnormalities lead dentist to make an early diagnostic of this syndrome. These dental abnormalities can cause physiological and psychological disorders. Oral management includes oral hygiene education, prevention, conservative dental management and prosthetic rehabilitations. This paper describes the different prosthetic stages of oral rehabilitation in a 7-year-old child with Christ-Siemens-Touraine ectodermal dysplasia.